Keywords
hereditary factor VII deficiency
FVII
hypoproconvertinemia
coagulopathy
cholecystectomy
bleeding
FVII
hypoproconvertinemia
coagulopathy
cholecystectomy
bleeding
Full Text
Abstract
Summary. The article presents the experience of perioperative management of a patient with severe congenital factor (F) VII deficiency during laparoscopic cholecystectomy at the First City Clinical Hospital named after E.E.Volosevich (Arkhangelsk). This clinical case demonstrates the choice of the optimal method for perioperative management of a patient with severe congenital FVII deficiency during surgery. The article presents information on the pathophysiology, diagnosis of FVII mutation, an algorithm for diagnosing hereditary coagulopathy — hypoproconvertinemia based on literature data and in real clinical practice, and perioperative management strategy.
For citation: VorobyevaN.A., VorobyevaA.I., VorontsovaA.S., BykovaN.V. Perioperative management of a patient with hereditary hypoproconvertinemia.Tromboz, gemostaz i reologiya. 2025;(2):122–128. (In Russ.).
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